Ataxia telangiectasia: why should the ERS care?

Jayesh M. Bhatt*, Andrew Bush, Marjo van Gerven, Andreea Nissenkorn, Michael Renke, Lian Yarlett, Malcolm Taylor, Thorny Tonia, Adilia Warris, Stefan Zielen, Shairbanu Zinna, Peter J. F. M. Merkus

*Corresponding author for this work

Research output: Contribution to journalEditorial

3 Citations (Scopus)

Abstract

Neurological and immunological contributions to lung disease in A-T require proactive and multidisciplinary management http://ow.ly/TqT44

Why indeed should we care? The answer is that ataxia telangiectasia (A-T) patients will present to respiratory paediatricians for diagnosis, when standard testing, if the diagnosis is not made, may do irreparable harm; and both adult and paediatric respiratory physicians will be involved in managing the respiratory disease, which is a major cause of morbidity and mortality. So there is a real “need to know” which is why the ERS convened a task force on A-T, whose findings are published in the European Respiratory Review [1].
Original languageEnglish
Pages (from-to)1557-1560
Number of pages4
JournalEuropean Respiratory Journal
Volume46
Issue number6
Early online date30 Nov 2015
DOIs
Publication statusPublished - 1 Dec 2015

Keywords

  • lung-disease
  • nutritional-status
  • immunodeficiency
  • infections
  • deficiency
  • child

Cite this

Bhatt, J. M., Bush, A., van Gerven, M., Nissenkorn, A., Renke, M., Yarlett, L., ... Merkus, P. J. F. M. (2015). Ataxia telangiectasia: why should the ERS care? European Respiratory Journal, 46(6), 1557-1560. https://doi.org/10.1183/13993003.01456-2015

Ataxia telangiectasia : why should the ERS care? / Bhatt, Jayesh M.; Bush, Andrew; van Gerven, Marjo; Nissenkorn, Andreea; Renke, Michael; Yarlett, Lian; Taylor, Malcolm; Tonia, Thorny; Warris, Adilia; Zielen, Stefan; Zinna, Shairbanu; Merkus, Peter J. F. M.

In: European Respiratory Journal, Vol. 46, No. 6, 01.12.2015, p. 1557-1560.

Research output: Contribution to journalEditorial

Bhatt, JM, Bush, A, van Gerven, M, Nissenkorn, A, Renke, M, Yarlett, L, Taylor, M, Tonia, T, Warris, A, Zielen, S, Zinna, S & Merkus, PJFM 2015, 'Ataxia telangiectasia: why should the ERS care?', European Respiratory Journal, vol. 46, no. 6, pp. 1557-1560. https://doi.org/10.1183/13993003.01456-2015
Bhatt JM, Bush A, van Gerven M, Nissenkorn A, Renke M, Yarlett L et al. Ataxia telangiectasia: why should the ERS care? European Respiratory Journal. 2015 Dec 1;46(6):1557-1560. https://doi.org/10.1183/13993003.01456-2015
Bhatt, Jayesh M. ; Bush, Andrew ; van Gerven, Marjo ; Nissenkorn, Andreea ; Renke, Michael ; Yarlett, Lian ; Taylor, Malcolm ; Tonia, Thorny ; Warris, Adilia ; Zielen, Stefan ; Zinna, Shairbanu ; Merkus, Peter J. F. M. / Ataxia telangiectasia : why should the ERS care?. In: European Respiratory Journal. 2015 ; Vol. 46, No. 6. pp. 1557-1560.
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